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A desmoid tumor (sometimes referred to as aggressive fibromatosis) is a rare (3 per million population) tumor that may or may not be part of a genetic syndrome such as familial adenomatous polyposis (FAP).
The superficial form is also known as Dupuytren's fibromatosis, and is small and slow-growing, rarely involving deeper structures. Deep fibromatosis is more aggressive. Histologically they resemble low-grade fibrosarcomas, but they are very infiltrative and tend to recur even after complete resection (systemic metastasis is rare).
Desmoid tumors may be classified as extra-abdominal, abdominal wall, or intra-abdominal (the last is more common in patients with FAP). The lesions may develop in relation to estrogen or abdominal trauma/operations.
Treatment consists of complete surgical removal, but radiation therapy, antiestrogens and NSAIDs, or chemotherapy may be used.
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"Desmoid tumor"